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Preview	Issue Date	Title	Author(s)
	2002	Mucopolysaccharidosis type VI (Maroteaux-Lamy syndrome): A Y210C mutation causes either altered protein handling or altered protein function of N-acetylgalactosamine 4-sulfatase at multiple points in the vacuolar network	Bradford, T.; Litjens, T.; Parkinson, E.; Hopwood, J.; Brooks, D.
	2003	Family 39 a-L-iduronidases and b-D-xylosidases react through similar glycosyl-enzyme intermediates: Identification of the human iduronidase nucleophile	Nieman, C.; Wong, A.; He, S.; Clarke, L.; Hopwood, J.; Withers, S.
	1998	Two-dimensional mapping and microsequencing of lysosomal proteins from human placenta	Chataway, T.; Whittle, A.; Lewis, M.; Bindloss, C.; Davey, R.; Moritz, R.; Simpson, R.; Hopwood, J.; Meikle, P.
	2001	Conditional tissue-specific expression of the acid α-glucosidase (GAA) gene in the GAA knockout mice: implications for therapy	Raben, N.; Lu, N.; Nagaraju, K.; Rivera, Y.; Lee, A.; Yan, B.; Byrne, B.; Meikle, P.; Umapathysivam, K.; Hopwood, J.; Plotz, P.
	2001	Glycosidase active site mutations in human a-L-iduronidase	Brooks, D.; Fabrega, S.; Hein, L.; Parkinson, E.; Durand, P.; Yogalingam, G.; Matte, U.; Giugliani, R.; Dasvarma, A.; Eslahpazire, J.; Henrissat, B.; Mornon, J.; Hopwood, J.; Lehn, P.
	2001	Gentamicin-mediated suppression of Hurler syndrome stop mutations restores a low level of a-L-iduronidase activity and reduces lysosomal glycosaminoglycan accumulation	Keeling, K.; Brooks, D.; Hopwood, J.; Li, P.; Thompson, J.; Bedwell, D.
	1997	Novel Mutations in Sanfilippo A Syndrome : Implications For Enzyme Function	Weber, B.; Guo, X.H.; Wraith, J.; Cooper, A.; Kleijer, W.; Bunge, S.; Hopwood, J.
	2004	Glycosaminoglycan degradation fragments in mucopolysaccharidosis I	Fuller, M.; Meikle, P.; Hopwood, J.
	1999	Regulation of N-acetylgalactosamine 4-sulfatase expression in retrovirus-transduced feline mucopolysaccharidosis type VI muscle cells	Yogalingam, G.; Muller, V.; Hopwood, J.; Anson, D.
	1996	Structure and sequence of the human sulphamidase gene	Karageorgos, L.; Guo, X.H.; Blanch, L.; Weber, B.; Anson, D.; Scott, H.; Hopwood, J.